Bilaga 5 - Klassifikation av MDS/MPN
Tabell 1. Klassifikation enligt WHO 2016 [47, 48]
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Myelodysplastiska/myeloproliferativa neoplasier (MDS/MPN) |
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Kronisk myelomonocytleukemi (KMML) |
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Atypisk KML (aKML; BCR-ABL1-neg) |
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Juvenil myelomonocytleukemi (JMML) |
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MDS/MPN med ringsideroblaster och trombocytos (MDS/MPN-RS-T) |
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MDS/MPN, oklassificerbar (MDS/MPN-U) |
Tabell 2. Klassifikation enligt WHO 2022, 5th edition (Khoury, 2022) 2
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Myelodysplastiska/myeloproliferativa neoplasier (MDS/MPN) |
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Chronic myelomonocytic leukemia
CMML-1: < 5 % blast + promonocytes in PB and < 10 % in BM CMML-2: 5–19 % blast + promonocytes in PB and 10–19 % in BM |
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Myelodysplastic/myeloproliferative neoplasms with neutrophilia |
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Myelodysplastic/myeloproliferative neoplasms with SF3B1 and thrombocytosis |
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Myelodysplastic/myeloproliferative neoplasms, not otherwise specified |
Tabell 3. Klassifikation enligt ICC (Arber 2022)[3]
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Myelodysplastiska/myeloproliferativa neoplasier (MDS/MPN) |
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Clonal cytopenia with monocytosis of undetermined significance (CCMUS) |
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Clonal monocytosis of undetermined significance (CMUS) |
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Chronic myelomonocytic leukemia |
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Atypical chronic myeloid leukemia |
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Myelodysplastic/myeloproliferative neoplasm with thrombocytosis and SF3B1 mutation |
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Myelodysplastic/myeloproliferative neoplasm with ring sideroblasts and thrombocytosis, not otherwise specified |
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Myelodysplastic/myeloproliferative neoplasm, not otherwise specified |